Extragnathic sino-orbital myxoma: An extremely rare tumor at an even rarer site

Abstract

Myxomas are rare benign tumors of primitive mesenchymal origin that usually arise from the soft tissues and occasionally from the bones. Bony myxomas predominantly arise from the jaw bone and hence are also known as gnathic myxomas. Any other bony myxomas are termed as extragnathic. In view of rarity, uncertain histogenesis, nonspecific clinical features, confusing terminology, and unclear management protocols, the backbone of diagnosis is a thorough histopathologic examination. Only 2 reports on myxomas arising from the frontal sinus have been documented previously. A young man presented with proptosis secondary to a sino-orbital mass lesion arising from the frontal sinus. The patient underwent complete excision biopsy and bone curettage. Following excision, the patient is symptom free at 6 months of follow up and showed no evidence of recurrence.