Ligneous conjunctivitis in a Dandy-Walker syndrome: A rare case report
Ligneous conjunctivitis in a Dandy-Walker syndrome: A rare case report
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Date
2019-01-01
Authors
Srirampur, Arjun
Ramappa, Muralidhar
Chaurasia, Sunita
Vemuganti, Geeta
Journal Title
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Abstract
Ligneous conjunctivitis (LC) is a rare form of pseudomembranous conjunctivitis seen in children, perhaps due to plasminogen deficiency, which manifest as a chronic refractory pseudomembranous conjunctivitis. LC cases are incapable in maintaining their fibrinolytic activity due to plasminogen deficiency; consequently, transudates of plasma assume as a thick, gelatinous, woody membranes over the mucosal surfaces. This is a short case report on a child with a LC, who presented with recurrent pseudomembranous conjunctivitis in conjunction with progressive congenital hydrocephalus due to aqueductal stenosis (Dandy-Walker syndrome). This rare association was clinically confirmed and prompt corrective surgical measures were institute.d.
Description
Keywords
Dandy-Walker syndrome,
hydrocephalus,
ligneous conjunctivitis
Citation
Indian Journal of Ophthalmology. v.67(1)